Fig. 1

Serum acylcarnitines (A-D) and urine organic acids (E–H) in GSDIa patients and control groups. For all metabolites mean value is shown for each group of participants. C1: controls who had blood collection after the same fasting time as their matched patients (adults: n = 6, children: n = 4). C14: miristoylcarnitine; C16: palmitoylcarnitine; C18: stearoylcarnitine * p < 0.05; ** p < 0.01; ***p < 0.001